J Korean Pediatr Soc.  2000 Nov;43(11):1458-1464.

Study of Congenital Mitral Stenosis Cases Requiring Surgical Correction in the First 2-Years of Life

• Park IS
• Lee YS
• Han MY
• Lee JY
• Kim SJ
• Jo DJ
• Oh MH
• Kim WH
• Lee YT
• Bae EJ
• Kim SH

Abstract

PURPOSE: Congenital mitral stenosis(CMS) is a rare anomaly accounting for 0.4-0.5% of total heart disease. CMS which cases needed surgical correction in infancy are even rare. In this study, we analyzed 11CMS patients of less than 2 year of age who needed surgical corrections, in order to find out their diagnoses, the characteristics, the results of operation and prognoses, and the progress of disease without surgical correction.
METHODS
Retrospective studies were performed on eleven CMS patients of less than 2 years of age admitted to Sejong General Hospital between Jan. 1989 and Aug. 1999.
RESULTS
The surgeries were performed on 9 out of 11 enrolled patients. The median age was 8(3-20) months and the median weight was 5(4-9)kg. The mitral valves of the patients were classified anatomically as supramitral ring(4), parachute mitral valve(3), "typical" symmetric hypoplastic mitral valve(2) and asymmetric hypoplastic mitral valve(2). Three patients died after the surgical correction. Among them, fibroelastosis of left ventricle was found during the surgery in two cases, and the other case was considered to be in Eisenmenger state. 5. Reoperations were performed on 3 out of 6 surviving patients. While one case was an early reoperation, two case were late ones.
CONCLUSION
The patients with severe CMS under the age of two can be surgically corrected with an acceptable success rate. Poor results were observed, however, if the decisions for surgical intervention were delayed.

Keyword

Congenital mitral stenosis

MeSH Terms

Diagnosis
Heart Diseases
Heart Ventricles
Hospitals, General
Humans
Mitral Valve
Mitral Valve Stenosis*
Prognosis
Reoperation
Retrospective Studies