J Korean Ophthalmol Soc.  1986 Aug;27(4):729-734.

A Case of Gronblad-Strandberg Syndrome

Affiliations
  • 1Department of Ophthalmology, Won-Kwang University, School of Medicine, Iri. Korea.

Abstract

Pseudoxanthoma elasticum associated with angioid streaks has been called rthe Gronblad-Strandberg Syndrome. A 30-year-old female patient showed circumscribed, cream-colored, crepelike, redundant plaques on neck, axillae, periumbilical area, and inguinal regions. The histopathologic findings of the skin taken from the axilla revealed extensive basophilic degeneration of the elastic tissue and calcium deposition in the middle and lower dermis. Both fundi showed irregular angioid streaks radiating from the optic disk on ophthalmoscopy, and hyperfluorescence of angioid streaks was noted with fluorescein angiography.


MeSH Terms

Adult
Angioid Streaks
Axilla
Basophils
Calcium
Dermis
Elastic Tissue
Female
Fluorescein Angiography
Humans
Neck
Ophthalmoscopy
Optic Disk
Pseudoxanthoma Elasticum*
Skin
Calcium
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