J Korean Ophthalmol Soc.
1986 Aug;27(4):729-734.
A Case of Gronblad-Strandberg Syndrome
- Affiliations
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- 1Department of Ophthalmology, Won-Kwang University, School of Medicine, Iri. Korea.
Abstract
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Pseudoxanthoma elasticum associated with angioid streaks has been called rthe Gronblad-Strandberg Syndrome. A 30-year-old female patient showed circumscribed, cream-colored, crepelike, redundant plaques on neck, axillae, periumbilical area, and inguinal regions. The histopathologic findings of the skin taken from the axilla revealed extensive basophilic degeneration of the elastic tissue and calcium deposition in the middle and lower dermis. Both fundi showed irregular angioid streaks radiating from the optic disk on ophthalmoscopy, and hyperfluorescence of angioid streaks was noted with fluorescein angiography.