A Case of Simultaneous Correction of Frontoethmoidal Meningoencephalocele and Hypertelorism

Kim, Han Kyeol; Park, Jin Hyung; Lee, Jung Hoon; Chung, Seung Moon

Abstract

PURPOSE: A meningoencephalocele is a congenital malformation involving herniation of the meninges and cerebral tissue through a defect in the skull. For the patient with frontoethmoidal meningoencephalocele with hypertelorism, the removal of the meningoencephalocele without correction of the combined hypertelorism is not enough for getting a good cosmetic appearance. Correction of the hypertelorism is needed for cosmetic problem. We experienced a case of simultaneous correction of frontoethmoidal meningoencephalocele with hypertelorism.
METHODS
The meningoencephalocele was removed and the hypertelorism was corrected by central segment technique. The bone defects were filled with autogenous bone dusts. And the nose was reconstructed by a calvarial bone graft.
RESULTS
The patient had a good cosmetic appearance without any neurological complications without serious complications.
CONCLUSION
We experienced a case of simultaneous correction of frontoethmoidal meningoencephalocele with hypertelorism. And a brief review of related literatures is given.