J Korean Rheum Assoc.  2010 Mar;17(1):71-75. 10.4078/jkra.2010.17.1.71.

A Case of Abdominal Aortic Pseudoaneurysm That Was Treated with Inserting an Endovascular Stent Graft in a Patient with Behcet's Disease

• Son KM
• Kim IJ
• Kim HA
• Jeon EY
• Seo YI

• KMID: 2201996
• DOI: http://doi.org/10.4078/jkra.2010.17.1.71

Abstract

Behcet's disease is a chronic inflammatory disease of an unknown etiology, and it is characterized by recurrent oral and genital ulcerations, eye lesions skin lesions, and other involvement such as gastrointestinal ulcerations and lesions of the central nervous system and major vessels. The vascular lesions include deep vein thrombosis, superficial thrombophlebitis, arterial aneurysm and arterial occlusion. Aortic aneurysm or pseudoaneurysm is a rare complication, but it is one of the most common causes of death in Behcet's disease. We report here on a case of a 43 year old female with Behcet's disease that was complicated by an abdominal aortic pseudoaneurysm, and this was all successfully treated with percutaneous endovascular stent graft insertion, steroid pulse therapy and azathioprine.

Keyword

Behcet's disease; Aortic pseudoaneurysm; Stent graft

MeSH Terms

Aneurysm
Aneurysm, False
Aortic Aneurysm
Azathioprine
Cause of Death
Central Nervous System
Eye
Female
Humans
Skin
Stents
Thrombophlebitis
Transplants
Ulcer
Venous Thrombosis
Azathioprine

Figure

• 

  Fig. 1. The abdominal CT: (A) On admission, a 4×2.5×3 cm sized, abdominal pseudoaneurysm was seen at the infra abdominal aorta. (B) The abdominal pseudoaneurysm disappeared 27 months later.

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  Fig. 2. The reconstructed CT angiogram shows a successfully inserted stent graft in the infrarenal aortic area.

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