J Korean Pediatr Cardiol Soc.  2007 Sep;11(3):235-239.

Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery : Report of an Adult Case

Affiliations
  • 1Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea. jgynhg@dreamwiz.com
  • 2Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University, Seoul, Korea.

Abstract

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), also termed Bland-White-Garland syndrome, is a rare congenital cardiac anomaly characterized by myocardial ischemia which becomes symptomatic during early infancy leading to infarction, left heart failure or even death. More than 90% of patients can be dead within first year of life if untreated, so adult type ALCAPA without surgical correction is quitely rare. We present a case of a 20-year-old man with ALPACA syndrome whose diagnosis took several years to be made because he was mistaken to have organic mitral regurgitation.

Keyword

Anomalous origin of the left coronary artery from the pulmonary artery; Bland-White-Garland syndrome; Adult

MeSH Terms

Adult*
Bland White Garland Syndrome
Camelids, New World
Coronary Vessels*
Diagnosis
Heart Failure
Humans
Infarction
Mitral Valve Insufficiency
Myocardial Ischemia
Pulmonary Artery*
Young Adult
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