J Korean Pediatr Cardiol Soc.
2007 Sep;11(3):235-239.
Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery : Report of an Adult Case
- Affiliations
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- 1Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea. jgynhg@dreamwiz.com
- 2Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University, Seoul, Korea.
Abstract
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Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), also termed Bland-White-Garland syndrome, is a rare congenital cardiac anomaly characterized by myocardial ischemia which becomes symptomatic during early infancy leading to infarction, left heart failure or even death. More than 90% of patients can be dead within first year of life if untreated, so adult type ALCAPA without surgical correction is quitely rare. We present a case of a 20-year-old man with ALPACA syndrome whose diagnosis took several years to be made because he was mistaken to have organic mitral regurgitation.