J Korean Neurosurg Soc.  2015 Jun;57(6):440-444. 10.3340/jkns.2015.57.6.440.

Cognitive Outcome of Pediatric Moyamoya Disease

• Shim KW
• Park EK
• Kim JS
• Kim DS

• KMID: 2191252
• DOI: http://doi.org/10.3340/jkns.2015.57.6.440

Abstract

Quality of life is the current trend and issue for the most of human diseases. In moyamoya disease (MMD), surgical revascularization has been recognized as the possible assistance to reduce the neurological insult. However, the progressive nature of the disease has been invincible so far. To improve the quality of life of MMD patients not only the protection from the neurological insult but also the maintenance or improvement of cognitive function is inevitable. For pediatric MMD patients, younger age or longer duration of disease is the key factor among the prognostic factors for bad neurological outcomes. Hence, 'the earlier, the better' is the most precious rule for treatment. Protection from neurological insult is very critical and foremost important to improve cognitive outcome. Clinicians need to know the neuropsychological profile of MMD patients for the care of whole person and make an effort to protect the patients from neurological insults to maintain or improve it.

Keyword

Moyamoya disease; Cognitive outcome; Neuropsychological profile; Revascularization

MeSH Terms

Humans
Moyamoya Disease*
Quality of Life

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