J Korean Neurosurg Soc.  1996 Apr;25(4):856-860.

Congenital Dermal Sinus at Thoracic Region Associated

• Eun JP
• Jung N
• Kwon CY
• Zhang HY

Abstract

Congenital dermal sinus (CDS) is a rare entity widely known to occur as a result of the of the failure of the neuroectoderm to separate from the cutaneous ectoderm during the process of neurulation at the third to fifth week of gestation. The lesion can occur at any level of the craniospinal axis, but are located predominantly at the lumbosacral and occipital region. CDS of thoracic region and cervical region are rare. The patient with CDS presents with meningitis and/or mass effect from the associated inclusion tumor. They are usually dermoid or epidermoid cyst. Teratoma is rarely associated with CDS. We report our experience of CDS an 11-month old boy associated with an intramedullary dermoid tumor at the thoracic region, and together we report a review of the literature.

Keyword

Congenital dermal sinus; Craniospinal axis; Meningitis; Inclusion tumor; Thoracic region

MeSH Terms

Axis, Cervical Vertebra
Dermoid Cyst
Ectoderm
Epidermal Cyst
Humans
Infant
Male
Meningitis
Neural Plate
Neurulation
Pregnancy
Spina Bifida Occulta*
Teratoma