J Korean Neurol Assoc.
2004 Feb;22(1):67-70.
A Case of Adult-onset Rasmussen's Encephalitis Responsive to High-dose Steroid and Antiepileptic Medication
- Affiliations
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- 1Department of Neurology, Gangneung Asan Hospital, University of Ulsan College of Medicine, Korea. soonklee@knh.co.kr
- 2Department of Family Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
Abstract
- Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive unilateral hemispheric dysfunction as well as mental deterioration. Although the disorder typically begins in childhood, a few cases have been reported with symptom onset in adulthood showing variable clinical characteristics. We report a 63-year-old woman with adult-onset partial seizure with intermittent secondary generalization, progressive right hemiparesis, and aphasia, who showed positive response to high-dose steroid and antiepileptic drugs.