J Cardiovasc Ultrasound.  2012 Dec;20(4):213-215. 10.4250/jcu.2012.20.4.213.

Papillary Fibroelastoma Mimicking Vegetation of the Mitral Valve

• Kim SY
• Park TH
• Lee DY
• Lee DH
• Cho YR
• Kim MH
• Kim YD
• Hong SH

• KMID: 2177412
• DOI: http://doi.org/10.4250/jcu.2012.20.4.213

Abstract

Although cardiac papillary fibroelastoma is rare, it is the most common primary tumor of cardiac valves. The clinical presentation of these tumors varies from asymptomatic to embolic complications. We report an asymptomatic case of papillary fibroelastoma of mitral valve which was diagnosed by transthoracic echocardiography. The tumor was successfully resected by surgery.

Keyword

Papillary fibroelastoma; Mitral valve; Transthoracic echocardiography

MeSH Terms

Echocardiography
Heart Valves
Mitral Valve

Figure

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  Fig. 1 Transthoracic echocardiography shows a mobile and spherical mass of 1.0 cm in size attached to anterior mitral leaflet. Parasternal long axis view (A) and an apical four-chamberview (B).

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  Fig. 2 Gross specimen of excised mass reveals a friable mass with frond-like surface.

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  Fig. 3 Histological examination of the resected tumor showing papillary projection. The tumor surface is covered by a single layer of endocardial cells with an overlying thin layer of mucopolysaccharide matrix and an underlying acellular stroma composed of elastic fibers and collagen (Elastica van Gieson stain, × 40).

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