J Cardiovasc Ultrasound.  2012 Dec;20(4):189-192. 10.4250/jcu.2012.20.4.189.

Total Occlusion of Right Main Pulmonary Artery in a Patient with Takayasu's Arteritis and Severe Pulmonary Hypertension

• Choi HM
• Kim HK
• Shin HS
• Lee SA
• Lee HS
• Oh GC
• Lee SP
• Kim YJ
• Cho GY
• Sohn DW

• KMID: 2177406
• DOI: http://doi.org/10.4250/jcu.2012.20.4.189

Abstract

Takayasu's arteritis is a chronic inflammatory disorder that mainly involves medium to large sized arteries. Although pulmonary artery involvement is reported with a prevalence of about 10% to 50%, its clinical significance is underestimated. We report here one case of Takayasu's arteritis complicated by severe pulmonary hypertension due to right main pulmonary artery total occlusion.

Keyword

Tricuspid valve insufficiency; Takayasu's arteritis; Pulmonary arterial hypertension

MeSH Terms

Arteries
Humans
Hypertension, Pulmonary
Prevalence
Pulmonary Artery
Takayasu Arteritis
Tricuspid Valve Insufficiency
Hypertension, Pulmonary

Figure

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  Fig. 1 Chest radiography shows prominent left hilar opacity and right atrial enlargement.

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  Fig. 2 Transthoracic echocardiography. Ostium of right pulmonary artery was not clearly depicted in spite of the effort. RV: right ventricle, PA: pulmonary artery.

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  Fig. 3 Non-visualized right lung in lung perfusion scan.

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  Fig. 4 Computed tomographic pulmonary angiography. It shows occlusion of right main pulmonary artery (asterisk) and left main pulmonary artery stenosis (arrowhead).

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  Fig. 5 Coronary angiography reveals huge left circumflex coronary artery to right pulmonary artery fistula (arrowheads).

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  Supplemental Fig. 1 Arch aortography. It showed occluded left subclavian artery, left common carotid artery, and near total occlusion of right subclavian artery (arrowhead).

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