J Gynecol Oncol.  2008 Sep;19(3):202-204. 10.3802/jgo.2008.19.3.202.

A case of epithelioid sarcoma arising in the vulva

• Kim JH
• Choi YS
• Lee TS

• KMID: 2173404
• DOI: http://doi.org/10.3802/jgo.2008.19.3.202

Abstract

Epithelioid sarcoma of vulva is extremely rare. Only 20 cases have been reported in the literature so far. Early diagnosis is difficult because of its benign appearance as a painless subcutaneous nodule. Therefore treatment can be delayed, although epithelioid sarcoma requires prompt surgery. We report a case of epithelioid sarcoma that occurred in the left vulva with a brief review of literature.

Keyword

Epithelioid sarcoma; Vulva; Treatment

MeSH Terms

Early Diagnosis
Sarcoma
Vulva

Figure

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  Fig. 1 Magnetic resonance image shows 1 cm size soft tissue mass in the left vulvar area (arrow).

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  Fig. 2 Microscopic findings show epithelioid cells, spindle or polygonal cell components with atypia (A)(H&E, ×400). Immunohistochemistry show positive for cytokeratin (B) and vimentin (C)(×400).

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