Chonnam Med J.  2009 Apr;45(1):70-72. 10.4068/cmj.2009.45.1.70.

A Case of Huge Mediastinal Cavernous Lymphangioma

• Jeon JK
• Na KJ
• Song SY

• KMID: 2172287
• DOI: http://doi.org/10.4068/cmj.2009.45.1.70

Abstract

Mediastinal lymphangioma is a rare benign lesion and mostly asymptomatic and usually found accidentally in childhood. We experienced a case of huge mediastinal cystic mass which occupied the whole left hemithorax in a 2-year-old male patient presenting cough and tachypnea. The tumor was completely resected by means of posterolateral thoracotomy. Pathological diagnosis confirmed cavernous lymphangioma. There is no evidence of tumor recurrence for 24 months postoperatively.

Keyword

Mediastinal neoplasms; Lymphangioma

MeSH Terms

Caves
Cough
Humans
Lymphangioma
Male
Mediastinal Cyst
Mediastinal Neoplasms
Preschool Child
Recurrence
Tachypnea
Thoracotomy

Figure

• 

  Fig. 1 Radiologic finding of Cavernous lymphangioma in 2-year-old male. (A) Chest X-ray shows a homogenous opacity on left thorax and rightward displacement of mediastinal structures, (B) Chest CT demonstrates a huge multi-septated cystic mass occupying left hemithorax with water-like density, (C) Chest CT shows total atelectasis of left lung.

• 

  Fig. 2 Pathologic finding of Cavernous lymphangioma in 2-year-old male. (A) Thin-walled, dilated lymphatic vessels of different size are surrounded by smooth muscle layer and lymphocytic aggregates (H-E stain, ×100), (B) Lymphatic vessel is lined by a flattened endothelium (H-E stain ×500), (C) Endothelial cells of the lumen are positive for CD31 (×250), (D) Endothelial cells of the lumen are positive for D2-40 (×250).

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