Ann Surg Treat Res.  2015 Oct;89(4):220-223. 10.4174/astr.2015.89.4.220.

Onset of adrenal ganglioneuroblastoma in an adult after delivery

• Qiu W
• Li T
• Sun XD
• Lv GY

• KMID: 2166898
• DOI: http://doi.org/10.4174/astr.2015.89.4.220

Abstract

A case of adrenal ganglioneuroblastoma is presented here. This adrenal ganglioneuroblastoma was found in a 27-year-old female 7 months after delivery. CT clarified that the tumor originated retroperitoneally and was large in size (11.4 cm x 9.4 cm). The tumor was surgically removed together with pancreatic body and tail, left kidney and spleen, and pathological diagnosis was adrenal ganglioneuroblastoma-intermixed. Adrenal ganglioneuroblastoma is extremely rare in adults, with only about 9 cases documented including this case.

Keyword

Ganglioneuroblastoma; Adult; Adrenal glands

MeSH Terms

Adrenal Glands
Adult*
Diagnosis
Female
Ganglioneuroblastoma*
Humans
Kidney
Spleen
Tail

Figure

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  Fig. 1 Computed tomographic images and gross examination of tumor. (A) Arterial phase, (B) venous phase, (C) delayed phase, and (D) gross pathologic specimens.

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  Fig. 2 Histologic examination and Immunohistochemistry of resected specimen. (A) Gangliocytes and neuroblasts showed in tumor (H&E): (1) gangliocytes (×200), (2) gangliocytes (×400), (3) neuroblasts (×200), (4) neuroblasts (×400); (B) CgA, Syn, and NF expressed in tumor (Immunohistochemistry): (1) CgA (magnification, ×400), (2) Syn (magnification, ×400), and (3) NF (magnification, ×400).

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