Ann Dermatol.  2011 Oct;23(Suppl 2):S258-S260. 10.5021/ad.2011.23.S2.S258.

Steatocystoma Multiplex Confined to the Scalp with Concurrent Alopecia

• Lee D
• Chun JS
• Hong SK
• Seo JK
• Choi JH
• Koh JK
• Sung HS

• KMID: 2156804
• DOI: http://doi.org/10.5021/ad.2011.23.S2.S258

Abstract

Steatocystoma multiplex (SM) is an uncommon disorder of the pilosebaceous unit characterized by the development of numerous sebum-containing dermal cysts which rarely involves the scalp. Here, we report a case of a 50-year-old man with multiple cystic nodules and alopecic patches on his scalp. On histopathological examination, the folded cyst was found to be lined by stratified squamous epithelium, while flattened sebaceous gland cells were identified in the cystic wall. Pigment casts were present in the hair papillae and perifollicular regions, suggesting trichotillomania as a possible cause of the observed alopecia. This case appears to represent an unusual clinical manifestation of SM.

Keyword

Alopecia; Scalp; Steatocystoma multiplex

MeSH Terms

Alopecia
Epithelium
Hair
Humans
Middle Aged
Scalp
Sebaceous Glands
Steatocystoma Multiplex
Trichotillomania

Figure

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  Fig. 1 A 50-year-old man presented with asymptomatic multiple cystic nodules (ranging in size from 2 mm to 4 cm) and alopecic patches on his scalp.

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  Fig. 2 (A) The cyst was located within the lower dermis and subcutaneous fat (H&E, ×12.5). The folded cystic wall was lined by stratified squamous epithelium and contained flattened sebaceous gland cells (inset) (H&E, ×400). (B) Pigment casts were present in the hair papillae and peribulbar connective tissue (H&E, ×100).

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