Ann Dermatol.  2008 Dec;20(4):247-249. 10.5021/ad.2008.20.4.247.

A Case of Atrophia Maculosa Varioliformis Cutis

• Kim DH
• Lee SM
• Kim TY
• Yoon MS

• KMID: 2156406
• DOI: http://doi.org/10.5021/ad.2008.20.4.247

Abstract

Atrophia maculosa varioliformis cutis is a rare disease that was first described by Heidingsfeld in 1918. It is characterized by an idiopathic, non-inflammatory macular atrophy that typically occurs on the face in young individuals. Despite its association with some diseases, the etiopathogenesis of this entity remains unknown. After consideration of the differential diagnosis criteria for idiopathic atrophic conditions, we report a case for a 40-year-old Korean male whose past medical history was suggestive of atrophia maculosa varioliformis cutis.

Keyword

Atrophia maculosa varioliformis cutis; Face; Scar

MeSH Terms

Adult
Atrophy
Cicatrix
Diagnosis, Differential
Humans
Male
Rare Diseases

Figure

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  Fig. 1 Two well-demarcated skin-colored atrophic scars measuring 3×2 mm located on the right cheek.

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  Fig. 2 (A) Slightly atrophied epidermis and solar elastosis in the upper dermis (H&E, ×40). (B) Note the elastotic material in the superficial and mid-dermis (inset) (Verhoeff van Gieson, ×100)

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