Obstet Gynecol Sci.  2016 Jan;59(1):50-53. 10.5468/ogs.2016.59.1.50.

Successful pregnancy and delivery of a patient with congenital adrenal hyperplasia

• Mun DH
• Yun HN
• Kim JW
• Kim YH
• Song TB

• KMID: 2152644
• DOI: http://doi.org/10.5468/ogs.2016.59.1.50

Abstract

Congenital adrenal hyperplasia (CAH) during pregnancy is a rare condition. Only a few cases have been reported in the literature. CAH patients has lower pregnancy rate compared to normal women. A 27-year-old nulliparous woman, a diagnosed case of 21-hydroxylase deficient simple virilising form of classic CAH visited. She got pregnant spontaneously without any trial of assisted reproductive technology. At the age of 12, she underwent clitoral resection and vaginoplasty. She took dexamethasone or prednisolone after operation. She delivered healthy singleton female baby by cesarean section. Four years later, she delivered healthy singleton female baby by repeat cesarean section. Two female babies have shown normal external genitalia. Here, we report a case of successful pregnancy and delivery in a patient with CAH.

Keyword

Congenital adrenal hyperplasia; Delivery; Fertility; Pregnancy

MeSH Terms

Adrenal Hyperplasia, Congenital*
Adult
Cesarean Section
Cesarean Section, Repeat
Dexamethasone
Female
Fertility
Genitalia
Humans
Prednisolone
Pregnancy Rate
Pregnancy*
Reproductive Techniques, Assisted
Steroid 21-Hydroxylase
Dexamethasone
Prednisolone
Steroid 21-Hydroxylase

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