Ann Surg Treat Res.  2015 Dec;89(6):334-337. 10.4174/astr.2015.89.6.334.

Neonatal vitelline vein aneurysm with thrombosis: prompt treatment should be needed

• Kim SH
• Yu HW
• Kim HY
• Jo HS

• KMID: 2148310
• DOI: http://doi.org/10.4174/astr.2015.89.6.334

Abstract

Vitelline veins are a pair of embryonic structures. The veins develop the portal vein system. Serious problems occur if the vitelline vein does not regress and becomes an aneurysm. Thrombus formation in the vitelline vein aneurysm could lead to portal vein thrombosis and portal hypertension unless promptly and correctly treated. Though vitelline vein aneurysm is an extremely rare anomaly, it rapidly progresses to portal vein thrombosis that requires prompt diagnosis and treatment. We reported a case of neonatal vitelline vein aneurysm and thrombosis that was cured by prompt operation.

Keyword

Vitelline vein; Aneurysm; Thrombosis; Portal hypertension; Newborn infant

MeSH Terms

Aneurysm*
Diagnosis
Embryonic Structures
Humans
Hypertension, Portal
Infant, Newborn
Portal Vein
Thrombosis*
Veins*
Venous Thrombosis
Vitellins*
Vitellins

Figure

• 

  Fig. 1 Ultrasonographic findings on the day of birth: (A) an elongated aneurismal tubular structure (V: vitelline vein aneurysm) with connection to the main portal vein (PV) coursing towards the umbilicus (U), (B) Color Doppler ultrasonography showed patent portal vein flow.

• 

  Fig. 2 Three-dimensional CT abdominal findings: abnormal tubular dilatated vascular structure and intraluminal thrombus, vitelline vein aneurysm (black arrowheads), connected with superior mesenteric vein (white arrow), splenic vein (black arrow) and portal vein (white arrowheads).

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