Korean J Med.
1999 Nov;57(5):950-955.
Primary intimal saroma of the aorta
- Affiliations
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- 1Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.
Abstract
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Primary intimal sarcoma of the aorta is a rare disease and has poor prognosis due to the
difficulty of early diagnosis. Recently, we experienced a 42 year-old female patient who had
primary intimal sarcoma of the aorta with metastasis. She complained of claudication, abdominal
pain, flank pain and pulselessness. CT angiography showed thrombus-like lesion in the aorta.
In our case, the transesophageal echocardiographic findings were different from those of usual
thrombus, which suggested the importance of transesophageal echocardiography in the differential
diagnosis of intra-aortic mass. Exploration was done because of the highly mobile portion and
the biopsy revealed that the mass was intimal sarcoma. Immunohistochemical staining for actin
and vimentin was positive. She died of massive gastrointestinal bleeding during admission.
At autopsy, the sarcoma was found to metastasize into small intestine, kidney, and ovary.