Korean J Med.  1999 Nov;57(5):950-955.

Primary intimal saroma of the aorta

Affiliations
  • 1Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.

Abstract

Primary intimal sarcoma of the aorta is a rare disease and has poor prognosis due to the difficulty of early diagnosis. Recently, we experienced a 42 year-old female patient who had primary intimal sarcoma of the aorta with metastasis. She complained of claudication, abdominal pain, flank pain and pulselessness. CT angiography showed thrombus-like lesion in the aorta. In our case, the transesophageal echocardiographic findings were different from those of usual thrombus, which suggested the importance of transesophageal echocardiography in the differential diagnosis of intra-aortic mass. Exploration was done because of the highly mobile portion and the biopsy revealed that the mass was intimal sarcoma. Immunohistochemical staining for actin and vimentin was positive. She died of massive gastrointestinal bleeding during admission. At autopsy, the sarcoma was found to metastasize into small intestine, kidney, and ovary.

Keyword

Aorta; Sarcoma; Transesophageal echocardiography

MeSH Terms

Abdominal Pain
Actins
Adult
Angiography
Aorta*
Autopsy
Biopsy
Diagnosis, Differential
Early Diagnosis
Echocardiography
Echocardiography, Transesophageal
Female
Flank Pain
Hemorrhage
Humans
Intestine, Small
Kidney
Neoplasm Metastasis
Ovary
Prognosis
Rare Diseases
Sarcoma
Thrombosis
Vimentin
Actins
Vimentin
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