J Korean Child Neurol Soc.
2001 May;9(1):171-177.
A Case of Neurocutaneous Giant Melanosis Associated with Dandy-Walker Syndrome
- Affiliations
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- 1Department of Pediatrics, College of Medicine, Dong-A University, Pusan, Korea.
- 2Department of Diagnostic Radiology, College of Medicine, Dong-A University, Pusan, Korea.
Abstract
- Neurocutaneous melanosis is a rare congenital phacomatosis, characterized by the presence of multiple pigmented skin nevi at birth. Meningeal melanosis tending to become malignant and seizure. Dandy-Walker syndrome is a developmental disorder of brain characterized by cystic dilatation of the fourth ventricle and agenesis or hypoplasia of the cerebellar vermis. We studied a case of Dandy-Walker syndrome with neurocutaneous giant melanosis in a 3 years old boy.
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