J Korean Assoc Pediatr Surg.  2015 Dec;21(2):32-34. 10.13029/jkaps.2015.21.2.32.

Inguinal Ectopic Scrotum, Anorectal Malformation with Sacral Agenesis and Limb Defects: An Unusual Presentation

Affiliations
  • 1Department of Pediatric Surgery, Postgraduate Institute of Medical Education and Research (PGIMER), Chandigarh, India. monikabawa@hotmail.com

Abstract

A case of congenital ectopic scrotum in neonatal period is described. The ectopic scrotum was located in the right inguinal area and the left hemiscrotum was found in normal location and each hemi-scrotum contained their testis. The neonate also had imperforate anus as low anorectal malformation with spinal abnormalities (hemi-sacrum and hemi-pelvis), right knee flexion contracture and right club foot. The embryological explanation in the literature of ectopic scrotum and its associated anomalies is discussed.

Keyword

Ectopic; Scrotum; Sacral agenesis; Anorectal malformations

MeSH Terms

Anus, Imperforate
Contracture
Extremities*
Foot
Humans
Infant, Newborn
Knee
Scrotum*
Testis

Figure

  • Fig. 1 (A-C) Photographs show ectopic scrotum in the inguinal region with low anorectal malformation with sacral agenesis.


Reference

1. Sule JD, Skoog SJ, Tank ES. Perineal lipoma and the accessory labioscrotal fold: an etiological relationship. J Urol. 1994; 151:475–477.
2. Lamm DL, Kaplan GW. Accessory and ectopic scrota. Urology. 1977; 9:149–153.
3. Spears T, Franco I, Reda EF, Hernandez-Graulau J, Levitt SB. Accessory and ectopic scrotum with VATER association. Urology. 1992; 40:343–345.
4. Stephens FD. Embryology of the cloaca and embryogenesis of anorectal malformations. Birth Defects Orig Artic Ser. 1988; 24:177–209.
5. Sen KK, Patel M. Caudal regression syndrome. Med J Armed Forces India. 2007; 63:178–179.
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