J Korean Pediatr Soc.  1996 Feb;39(2):273-279.

Four Cases of Congenital Esophageal Stenosis Due to Tracheobronchial Remnants

• Sung GW
• Lee SY
• Choi YH
• Kim KM
• Seo JK
• Kim IW
• Park KW
• Kim JJ

Abstract

Esophageal stenosis due to tracheobronchial remnants is a rare cause of congenital esophageal stenosis. The cause is thought to be esophageal sequestration of tracheobronchial remnants during embryonic separation. Errors in diagnosis are common and high index of suspicion is required for accurate diagnosis, and resection of primary site with anastomosis is recommanded. Although a rare entity, esophageal stenosis due to tracheobronchial remnants should be considered in patients with esophageal stenosis, when esophageal stenosis fails to respond to standard therapy including bougienage and balloon dilatation, and esophagoscopy shows normal mucosa on the stenotic segment. Four cases of congenital esophageal stenosis due to tracheobronchial remnants were reported, the first case without accompanied anomaly, the second case accompanied by tracheoesophageal fistula, the third case accompanied by Down syndrome, and the last case accompanied by tracheoesophageal fistula and congenital heart disease.

Keyword

Tracheobronchial remnants; Congenital esophageal stenosis; Esophagoscopy; Tracheo esophageal fistula

MeSH Terms

Diagnosis
Dilatation
Down Syndrome
Esophageal Stenosis*
Esophagoscopy
Heart Defects, Congenital
Humans
Mucous Membrane
Tracheoesophageal Fistula