J Korean Soc Coloproctol.  2009 Feb;25(1):52-55. 10.3393/jksc.2009.25.1.52.

Rectal Involvement of Klippel-Trenaunay Syndrome

• Cheon SH
• Lee SH
• Park EB

• KMID: 2101473
• DOI: http://doi.org/10.3393/jksc.2009.25.1.52

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder and is essentially a disorder of capillary, venous, and lymphatic malformations. Hematochezia is the most common symptom associated with intestinal hemangiomatosis and remains one of the life-threatening emergencies in KTS. We reported one patient of KTS presented with rectal bleeding and severe anemia who was successfully managed by sphincter-saving operation.

Keyword

Rectal bleeding; Klippel-Trenaunay syndrome; Coloanal anastomosis

MeSH Terms

Anemia
Capillaries
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Emergencies
Gastrointestinal Hemorrhage
Hemorrhage
Humans
Klippel-Trenaunay-Weber Syndrome