J Lipid Atheroscler.  2013 Jun;2(1):41-44. 10.12997/jla.2013.2.1.41.

A Case of Periaortitis Diagnosed with Abdomen CT in a Patient with Malignant Fibrous Histiocytosis

• Moon SK
• Kim KH
• Kim HJ
• An HJ
• Lee SS
• Song HY
• Kang WY
• Cho SC
• Hwang SH
• Kim W

• KMID: 2095094
• DOI: http://doi.org/10.12997/jla.2013.2.1.41

Abstract

Periaortitis is a very rare disease, characterized by a fibro-inflammatory tissue which develops around abdominal aorta and iliac arteries, and spreads into the structures of retroperitoneum. Computed tomography (CT) or magnetic resonance imaging (MRI) is the modality of choice for the diagnosis. Here, we report a case of periaortitis diagnosed with abdomen CT in patient with malignant fibrous histiocytoma.

Keyword

Periaortitis; Retroperitoneal fibrosis; Malignant fibrous histiocytoma

MeSH Terms

Abdomen
Aorta, Abdominal
Histiocytoma, Malignant Fibrous
Histiocytosis
Humans
Iliac Artery
Magnetic Resonance Imaging
Rare Diseases
Retroperitoneal Fibrosis

Figure

• 

  Fig. 1 Initial computed-tomography (CT) and after 1 month of steroid treatment. (A) shows soft tissue lesion in periaortic area (infrarenal abdominal aorta) with delayed enhancement (arrow) and (B) shows follow-up CT, marked improvement of soft tissue lesion (arrow) in periaortic area.

• 

  Fig. 2 (A) shows microscopic appearance of spindle cell (thin arrow), pleomorphic cell (thick arrow) and myxoid background (H&E, ×200). (B) shows magnetic resonance imaging (MRI) that well defined, longitudinally elongated mass lesion with septation and heterogenous enhancement in pretibial muscle layer.

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