Korean J Anesthesiol.  2011 Nov;61(5):428-430. 10.4097/kjae.2011.61.5.428.

Anesthetic management of an adult patient with Rett syndrome and limited mouth opening: A case report

• Nho JS
• Shin DS
• Moon JY
• Yi JW
• Kang JM
• Lee BJ
• Kim DO
• Chung JY

• KMID: 2092326
• DOI: http://doi.org/10.4097/kjae.2011.61.5.428

Abstract

Rett syndrome is a neurological disease that occurs only in females and it manifests with mental retardation, seizures, movement disorders, autistic behavior and abnormal breathing. A 19-year-old female with Rett syndrome underwent ophthalmologic surgery under general anesthesia at our institution. Airway control was difficult due to her limited mouth opening. We recommend that anesthesiologists should have proper knowledge about this disease and the patients to avoid the complications and problems that can be encountered during the perioperative period.

Keyword

Bronchoscopic intubation; Limited mouth opening; Rett syndrome

MeSH Terms

Adult
Airway Management
Anesthesia, General
Female
Humans
Intellectual Disability
Mouth
Movement Disorders
Perioperative Period
Respiration
Rett Syndrome
Seizures
Young Adult