Korean J Dermatol.  2003 Sep;41(9):1210-1214.

A Case of Phakomatosis Pigmentovascularis Type I a With Multiple Pyogenic Granulomas Developed in Pregnancy

• Moon YJ
• Jang SJ
• Choi YH
• Won JY
• Jung GD

Abstract

Phakomatosis pigmentovascularis(PPV) was first described in 1947 as a distinctive association of vascular and pigmentary nevi by Ota et al. Hasegawa et al subclassified the disorder into eight types and type I a is characterized by the coexistence of nevus flammeus and nevus pigmentosus et verrucous, which is not associated with systemic organ involvement. PPV type I a is relatively rare and a case with multiple pyogenic granulomas developed in pregnancy, is not reported yet. We present a case of PPV type I a with multiple pyogenic granulomas developed in pregnancy within nevus flammeus in a 29-year-old female.

Keyword

Phakomatosis pigmentovascularis; Ppyogenic granuloma

MeSH Terms

Adult
Female
Granuloma, Pyogenic*
Humans
Neurocutaneous Syndromes*
Nevus
Port-Wine Stain
Pregnancy*