Korean J Med.  2005 Dec;69(6):692-695.

Budd-Chiari syndrome associated with diaphragmatic hernia: A case report

• Yun JW
• Park YB
• Kong H
• Jung SW
• Lee TK
• Song JM

Abstract

Budd-Chiari syndrome (BCS) is a rare disease caused by the obstruction of the hepatic venous outflow or the inferior vena cava above the hepatic vein. It has been attributed to various etiologic factors. Including intrinsic vascular thrombosis, hepatic tumor invasion/compression, or associated with an idiopathic obstructing membrane. However, in most cases no definitive etiologic factors have been identified. Recently, we experienced a case of 21-year-old man who had Budd-Chiari syndrome associated with diaphragmatic hernia. Venous flow returned to normal on reintroduction of the liver into the abdominal cavity and closure of the defect in the diaphragm. To our knowledge, this is the rare report in our country. Here, we report this case with review of literatures.

Keyword

Budd-Chiari syndrome; Hernia; Diaphragmatic

MeSH Terms

Abdominal Cavity
Budd-Chiari Syndrome*
Diaphragm
Hepatic Veins
Hernia
Hernia, Diaphragmatic*
Humans
Liver
Membranes
Rare Diseases
Thrombosis
Vena Cava, Inferior
Young Adult