Korean J Thorac Cardiovasc Surg.  2010 Oct;43(5):518-521.

Right Ventricle Exclusion in Severe Neonatal Ebstein's Anomaly

Affiliations
  • 1Department of Thoracic and Cardiovascular Surgery, Seoul Paik Hospital, Inje University School of Medicine, Korea.
  • 2Department of Thoracic and Cardiovascular Surgery, College of Medicine, Seoul National University, Korea. woonghan@snu.ac.kr

Abstract

A one-day-old baby was transferred for cyanosis and heart murmur. Echocardiographic evaluation revealed that he had severe neonatal Ebstein's anomaly (Carpentier type C), pulmonary atresia, and pulmonary circulation via patent ductus arteriosus. Because the wall of the atrialized right ventricle was very thin, showed decreased contractility, and the small right ventricle showed pulmonary atresia, we decided that a two-ventricular repair was impossible. When the patient was one-month-old, he underwent right atrium reduction-plasty, a right ventricular exclusion procedure (including atrialized right ventricle resection and functional right ventricle plication), and right modified Blalock-Taussig shunt. He was discharged without specific problems. He received a bidirectional cavopulmonary shunt successfully at 4 months later.

Keyword

Right ventricle; Congenital heart disease; Ebstein's anomaly

MeSH Terms

Blalock-Taussig Procedure
Cyanosis
Ductus Arteriosus, Patent
Ebstein Anomaly
Fontan Procedure
Heart Atria
Heart Murmurs
Heart Ventricles
Humans
Pulmonary Atresia
Pulmonary Circulation
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