Korean J Pathol.
1997 Nov;31(11):1233-1236.
Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy: Report of an autopsy case
- Affiliations
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- 1Department of Pathology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul 038-040, Korea.
- 2Department of Nephrology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul 038-040, Korea.
Abstract
- A 35-year-old man was admitted with a 20 day history of generalized edema and muscular weakness of the lower extremities. He was alert with a pale puffy face and an ejection murmur was heard at the cardiac apex. The electrocardiogram disclosed low voltage, first degree atrioventricular block, and a right bundle branch block. During the hospitalization an intractable diastolic hypotension developed, which measured 0 mmHg at the lowest point. At that time the echocardiogram revealed a dilated, akinetic right ventricle. Eventually a multiorgan failure developed and an autopsy following his death presented a fibrofatty replacement of the right ventricular myocardium. This might be a case of an arrhythmogenic right ventricular dysplasia/cardiomyopathy, which is usually characterized clinically by a ventricular tachycardia and may cause a sudden death in young adults.
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