J Korean Neurol Assoc.
1991 Mar;9(1):79-84.
Neurofibromatosis: Report of 2 cases
- Affiliations
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- 1Department of Neurology, University, Korea.
- 2Department of Pediatrics, Catholic University Medical College, Korea.
Abstract
- Bilateral acoustic neurofibrornatosis or neurofibrornatosis-2 is characterized by bilateral acoustic neurornas and it is thought to be genetically distinct from the neurohbrornatosis-1. Also called von Recklinghausen's neurofibrornatosis. We report 2 patients with neurofibrornatosis-2. Who showed progressive bilateral hearing loss, unsteady gait and headache.Neuroirnaging studies revealed bilateral cerebellopontine angle rnasses and biopsies confirmed the diagnosis.
