J Korean Assoc Maxillofac Plast Reconstr Surg.  2010 Jan;32(1):81-85.

LONG TERM FOLLOW-UP OF MULTIPLE ODONTOGENIC KERATOCYSTS ASSOCIATED WITH BASAL CELL NEVUS SYNDROME: A CASE REPORT

• Lee EY
• Kim KW

Abstract

Multiple jaw cysts are one of the most constant features of the basal cell nevus syndrome. Basal cell nevus syndrome is inherited as an autosomal dominant trait with variable expressiveness. This syndrome comprises a number of abnormalities such as multiple nevoid basal cell carcinomas of the skin, skeletal abnormalities as bifid rib and fusion of vertebrae, central nervous system abnormalities as mental retardation, eye abnormalities with multiple jaw cysts.

Keyword

Basal cell nevus syndrome; Multiple odontogenic keratocyst

MeSH Terms

Basal Cell Nevus Syndrome
Carcinoma, Basal Cell
Central Nervous System
Eye Abnormalities
Follow-Up Studies
Intellectual Disability
Jaw Cysts
Nevus
Odontogenic Cysts
Ribs
Skin
Spine