Korean J Urol.  2007 Nov;48(11):1174-1178. 10.4111/kju.2007.48.11.1174.

Primary Leiomyosarcoma of the Ureter

• Cho KH
• Hyun JH
• Chung HY
• Chang YS
• Han DS

• KMID: 1997097
• DOI: http://doi.org/10.4111/kju.2007.48.11.1174

Abstract

An 82-year-old woman was admitted to our hospital with a palpable mass in her right lower abdomen. The mass was enlarged and tender for the previous 3 months. Abdomen-pelvic computed tomographic scan demonstrated severe right hydroureteronephrosis and about an 8x8x9cm sized huge irregular shaped pelvic mass. Retrograde pyelography showed complete obstruction of the right middle ureter. En bloc resection of the mass and segmental resection of the ureter was performed. Pathologically, it was diagnosed primary leiomyosarcoma of the ureter. At 3 month postoperatively, there has been no recurrence or metastasis.

Keyword

Leiomyosarcoma; Ureter

MeSH Terms

Abdomen
Aged, 80 and over
Female
Humans
Leiomyosarcoma*
Neoplasm Metastasis
Recurrence
Ureter*
Urography

Figure

• 

  Fig. 1 Contrast enhanced computed tomographic scan shows delayed perfusion of the kidney and severe hydronephrosis, a hydroureter, (right (A)) and a huge irregular margined heterogeneous enhancing mass in the right pelvic cavity (B). The enhancing mass (empty arrow) seems to be of a retroperitoneal origin because the right ureter was compressed by the mass (C). Retrograde pyelography shows medial deviation and lower ureteral kinking and complete obstruction at the mid ureter (D).

• 

  Fig. 2 The size of the large solid tumor was 10.5x10x7cm. Its shape and surface were irregular. On sections, it showed a white fibrotic solid appearance. The normal ureteral structure was not shown.

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  Fig. 3 The tumor cells showed immunohistochemically positivety to actin (A) and desmin (B) It was composed of deeply eosinophilic intersecting fascicles (C) (H&E x40) and necrosis (D) (H&E x100). Mitotic figures (E) (H&E x200) were noted.

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