Korean J Anesthesiol.  2007 Mar;52(3):363-366. 10.4097/kjae.2007.52.3.363.

Anesthesia for a Patient with Osler-Weber-Rendu Syndrome : A case report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Korea Institute of Radiological & Medical Sciences, Seoul, Korea. suamlee@netian.co.kr

Abstract

Hereditary haemorrhagic telangiectasia (HHT), or Osler-Weber-Rendu syndrome is an autosomal dominant disorder characterized by recurrent epistaxis, mucocutaneous telangiectasias, and visceral involvement including arteriovenous malformations that may develop in any organ, especially in the lung, brain, liver and GI tract. Early screening and regular follow up of patients with HHT are important to minimize the risk of development of serious sequelae. We report a case of 46-year-old female patient who had "suspected HHT" and review the literature on this rare disease.

Keyword

arteriovenous malformation; hereditary haemorrhagic telangiectasia; Osler-Weber-Rendu syndrome

MeSH Terms

Anesthesia*
Arteriovenous Malformations
Brain
Epistaxis
Female
Follow-Up Studies
Gastrointestinal Tract
Humans
Liver
Lung
Mass Screening
Middle Aged
Rare Diseases
Telangiectasia, Hereditary Hemorrhagic*
Telangiectasis
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