Korean J Dermatol.  1975 Dec;13(4):299-303.

Multiple Neurilemomas Associated with Neurofibromatosis

• Kim ST
• Kwon KS
• Chung TA

Abstract

Multiple neurilerv,omas occurred i.n a 14-year-old boy with neurofibromatosis and right eye blindness. His father succumbed to neurofibromatosis at the age of 42. Histologically-proved neurilemornas and neurofibromas were noted on the face, neck, trunk and extremities, but no cafe au-Iait spots ohserved. There were nevus anemicus, hairy nevus and pigmented moles. The associated features in this patient includc muscular atrophies, weakness of the left hand, parest,hesia of the medial side of left forcarm and Dupuytrens contracture of left fourth finger.

MeSH Terms

Adolescent
Blindness
Dupuytren Contracture
Extremities
Fathers
Fingers
Hand
Humans
Male
Muscular Atrophy
Neck
Neurilemmoma*
Neurofibroma
Neurofibromatoses*
Nevus
Nevus, Pigmented