Korean J Perinatol.  2014 Mar;25(1):33-36. 10.14734/kjp.2014.25.1.33.

A Case of Cantrell's Syndrome with Left Ventricular Diverticulum in a Neonate

• Yang HK
• Kim AY
• Lim RK
• Park KH
• Byun SY

• KMID: 1917231
• DOI: http://doi.org/10.14734/kjp.2014.25.1.33

Abstract

Cantrell's syndrome is a rare congenital anomaly, consists of five malformations. There are the midline abdominal wall defect, the defect of sterna lower part, an agenesis of the anterior part of the diaphragm, an absence of the diaphragmatic pericardium, and the congenital intracardiac problem. We diagnosed Cantrell's syndrome with left ventricular diverticulum in a female neonate with no perinatal problems. She experienced an one-staged operation and discharged with no complications. We report a case with brief review of the literature.

Keyword

Cantrell's syndrome; Ventricular diverticulum; One-staged operation

MeSH Terms

Abdominal Wall
Diaphragm
Diverticulum*
Female
Humans
Infant, Newborn*
Pericardium

Figure

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  Fig. 1. This image of the patient shows pulsating and protruding mass on the lower sternal area with abdominal wall defect to umbilicus.

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  Fig. 2. The abdominal ultrasound shows a defect of abdominal wall (A, arrow) and umbilical hernia (B, arrow).

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  Fig. 3. The Abdominal CT shows eventration of cardiac apex through dehiscent chest wall (A) and left ventricular diverticulum (B).

Reference

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