Korean J Thorac Cardiovasc Surg.  2002 Jul;35(7):556-559.

Combined Repair of Pectus Excavatum and Open Heart Surgery in Marfan's Syndrome

• Shin JK
• Jung JP
• Lee YJ

Abstract

The presense of pectus excavatum in Marfan's syndrome may complicate cardiac operation by making midline sternotomy technically more difficult and limiting the operative exposure of the heart. We operated on a 33 year old male patient with Marfan's syndrome and severe pectus excavatum who had severe mitral regurgitation and moderate aortic regurgitation with 52mm aortic root dilation. The operative field was adequately exposed through a midline sternal incision with two sternal retactors. The patient underwent Bentall operation and mitral valve replacement. The repair of pectus excavatum was performed after completion of CPB and the administration of protamin. Permanent internal stabilization achieved by overlapping of the ends of lower ribs and reinforced with sternal closure wire.

Keyword

Funnel chest; Marfan's syndrome

MeSH Terms

Adult
Aortic Valve Insufficiency
Funnel Chest*
Heart*
Humans
Male
Marfan Syndrome*
Mitral Valve
Mitral Valve Insufficiency
Ribs
Sternotomy
Thoracic Surgery*