J Korean Neurosurg Soc.  2001 May;30(5):642-646.

A Case of Spinal Cord Compression Caused by Rhabdomyosarcoma of the Mediastinum Associated with Type I Neurofibromatosis(NF Type I)

Affiliations
  • 1Department of Neurosurgery, Wonju College of Medicine, Yonsei University, Wonju, Korea.
  • 2Department of Diagnostic Radiology, Wonju College of Medicine, Yonsei University, Wonju, Korea.
  • 3Department of Cardiothoracic Surgery, Wonju College of Medicine, Yonsei University, Wonju, Korea.
  • 4Department of Pathology, Wonju College of Medicine, Yonsei University, Wonju, Korea.

Abstract

A 12-years-old female admitted to the hospital with the complaint of pain on the right upper chest area which persisted about 1 month prior to admission. Cafe-au-lait spots of various size laying on a whole body and freckling on the axilla were found on physical examination. A huge mass was found on the plain chest X-ray and on chest MRI. The mass encroached thoracic spine, posterior rib, back muscles, and then into the neural canal and compressed thoracic spinal cord. On the 5th day of hospitalization, the patient complained tingling on the both legs and 2 days later, monoparesis on the right leg. Open thoracotomy and decompressive laminectomy was done to remove mass. Pathologic reports confirmed rhabdomyosarcoma, embryonal type.

Keyword

Type I neurofibromatosis; Rhabdomyosarcoma; Mediastinum

MeSH Terms

Axilla
Back Muscles
Cafe-au-Lait Spots
Female
Hospitalization
Humans
Laminectomy
Leg
Magnetic Resonance Imaging
Mediastinum*
Neural Tube
Paresis
Physical Examination
Rhabdomyosarcoma*
Rhabdomyosarcoma, Embryonal
Ribs
Spinal Cord Compression*
Spinal Cord*
Spine
Thoracotomy
Thorax
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