Korean Circ J.  2012 Oct;42(10):718-721. 10.4070/kcj.2012.42.10.718.

Familial Occurrence of Atrioventricular Nodal Reentrant Tachycardia in a Mother and Her Son

• Namgung J
• Kwak JJ
• Choe H
• Kwon SU
• Doh JH
• Lee SY
• Lee WR

• KMID: 1826472
• DOI: http://doi.org/10.4070/kcj.2012.42.10.718

Abstract

Atrioventricular nodal reentrant tachycardia (AVNRT), caused by a reentry circuit involving fast and slow atrioventricular nodal pathways, is one of the most common types of paroxysmal supraventricular tachycardias. While familial Wolff-Parkinson-White syndrome has been well recognized, familial AVNRT has been rarely reported. We report a familial occurrence of AVNRT in a mother and her son, who were symptomatic and successfully treated with radiofrequency catheter ablation of slow pathway.

Keyword

Tachycardia, atrioventricular nodal reentrant

MeSH Terms

Catheter Ablation
Humans
Mothers
Tachycardia, Atrioventricular Nodal Reentry
Tachycardia, Supraventricular
Wolff-Parkinson-White Syndrome

Figure

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  Fig. 1 The mother's (A and B) and her son's (C and D) fluoroscopic images of endocardial mapping catheters in the right anterior oblique view (RAO) and the left anterior oblique view (LAO). The duodecapolar catheter was not fully engaged into the distal coronary sinus in both patients. The mother's (E) and her son's (F) intracardiac electrogram of typical atrioventricular nodal reentrant tachycardia (slow-fast type). During tachycardia, atrial activation is earliest at the HIS region and simultaneous with the ventricular activation. The VA interval (measured from the onset of ventricular activation on the surface electrocardiography to the earliest deflection of the atrial activation in the HIS electrogram) of both patients was <70 msec. HIS: His bundle, RV: right ventricle, HRA: high right atrium, CS: coronary sinus, ABL: ablation, VA: ventriculo-atrial, HISd: HIS distal, HISm: HIS middle, HISd: HIS distal.

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  Fig. 2 The mother's (A) and her son's electrogram (B) during typical atrioventricular nodal reentrant tachycardia. Following cessation of ventricular entrainment pacing the tachycardia resumes with a V-A-V response and the values of the post-pacing interval minus the tachycardia cycle length were greater than 115 msec in both patients. HISd: HIS distal, HISm: HIS middle, HISd: HIS distal, HA: HIS-atrial interval.

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