J Korean Soc Neonatol.  2007 Nov;14(2):226-231.

Infantile Type Choledochal Cyst with Biliary Atresia: Report of two cases

Affiliations
  • 1Department of Pediatrics, College of Medicine, Catholic University, Seoul, Korea. sykim@catholic.ac.kr
  • 2Department of Radiology, College of Medicine, Catholic University, Seoul, Korea.
  • 3Department of Pathology, College of Medicine, Catholic University, Seoul, Korea.

Abstract

Choledochal cysts in neonates and young infants take two forms: the choledochal cyst associated with biliary atresia (CCBA) and the choledochal cyst in the absence of biliary atresia (CC). Infants in both groups usually have similar clinical symptoms at presentation, but management and prognosis are different. While early portoenterostomy is required for CCBA, cyst excision with hepaticojejunostomy or choledochojejunostomy is usually performed for CC. The former shows a relatively poor prognosis, and the latter shows a better prognosis. Two infants who presented with clinical features of neonatal cholestasis, and clinically suspected to have choledochal cysts, were found on imaging studies and surgery to have extrahepatic bile duct atresia in association with choledochal cysts.

Keyword

Choledochal Cyst; Biliary Atresia; Infant

MeSH Terms

Bile Ducts, Extrahepatic
Biliary Atresia*
Choledochal Cyst*
Choledochostomy
Cholestasis
Humans
Infant
Infant, Newborn
Prognosis
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