J Korean Med Sci.  2010 Aug;25(8):1241-1243. 10.3346/jkms.2010.25.8.1241.

Successful Vaginal Delivery of a Pregnant Woman with Cantrell's Pentalogy

• Moon KY
• Choe SA
• Park CW
• Park JS
• Jun JK
• Syn HC

• KMID: 1714052
• DOI: http://doi.org/10.3346/jkms.2010.25.8.1241

Abstract

Cantrell's Pentalogy is a rare condition that consists of defects involving the abdominal wall, lower sternum, anterior diaphragm, pericardium, and heart. In the literature to date, pregnant women with Cantrell's Pentalogy have not been discussed. We performed successful vaginal delivery of a 23-yr-old nulliparous, primigravid woman who had been diagnosed with this condition. Diagnosis was based on cardiac catheterization, angiography, and echocardiogram, and abdominopelvic CT. Vaginal delivery may be an option for women with Cantrell's Pentalogy and may be attempted with caution.

Keyword

Cantrell's Pentalogy; Vaginal Delivery

MeSH Terms

Abdominal Muscles/abnormalities
Abdominal Wall/abnormalities
*Abnormalities, Multiple
Diaphragm/abnormalities
Echocardiography
Female
Humans
Oligohydramnios/diagnosis
Pregnancy
*Pregnancy Complications
Pregnancy Outcome
Sternum/abnormalities
Tomography, X-Ray Computed
Young Adult

Figure

• 

  Fig. 1 A fibrous band is seen connecting epigastrium and umbilicus. The finger indicates the beating of left ventricular apical diverticulum beneath the lower sternum defect.

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  Fig. 2 Computerized tomography images.( A) A transverse view below diaphragm shows apical diverticulum of left ventricle (arrow). (B) Low sternum and diaphragm defect, and pericardium defect (arrows) are seen in coronal section. (C) Unlike the right lateral side, abdominal muscle is hardly seen around midline (arrows) and left lateral side.

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