Korean J Dermatol.  1979 Dec;17(6):463-467.

Monilethrix with Keratosis Pilaris

• Kim JH
• Park HS
• Cho CK

Abstract

Monilethrix is a rare hereditary disorder of hair which was described by smith in 1879. The scalp hair is most frequently affected but the body or sexual hair are rarely affected. The affected hair shows periodic constrictions that break easily, so the hair could not grow more than a few millimetere long. It is thought that the node of the affected hair is normal and the thin internodal segment is deficient in hair matrix. Keratosis pilaris is generally an associated feature. We experienced a case of monilethrix with keratosis pilaris. The 4 years old male patient with monilethrix affected only scalp hair with keratosis. The family history was non-contributory.

MeSH Terms

Child, Preschool
Constriction
Hair
Humans
Keratosis*
Male
Monilethrix*
Scalp