J Korean Cleft Palate-Craniofac Assoc.  2007 Apr;8(1):29-32.

Experience of Benign Multiple Symmetrical Lipomatosis

• Huh C
• Mun GH
• Lee SH
• Kim HJ
• Lim SY
• Hyon WS
• Bang SI
• Oh KS

Abstract

Benign symmetrical lipomatosis, also known as Madelung's disease, is a rare condition characterized by massive fatty deposits arranged symmetrically around the neck, shoulders, and arms. Patients usually complain of their cosmetic appearance, but treatment can be considered for decreased neck motion and/or aerodigestive problems. Surgical lipectomy and liposuction are treatment of choice, but recurrence is common. Because the distribution of the lesion tends to be wide and diffuse, single operation is not sufficient for improving contour and functional problems, especially in severely affected case. We experienced a progressed patient who suffered from limitation of neck motion, dyspnea including sleep apnea due to massive deposits on whole neck. We performed 2 staged operations for the purpose of removing as much lipomatous tissue as possible. After 2 staged excisions, patient's appearance and aerodigestive problems are much improved and recurrence is not observed.

Keyword

Lipomatosis; Madelung's disease

MeSH Terms

Arm
Dyspnea
Humans
Lipectomy
Lipomatosis
Lipomatosis, Multiple Symmetrical*
Neck
Recurrence
Shoulder
Sleep Apnea Syndromes