Clin Pediatr Hematol Oncol.  2008 Apr;15(1):33-37.

A Case of Cystic Nephroma in Childhood

Affiliations
  • 1Department of Pediatrics, Gachon University of Medicine and Science, Incheon, Korea. isjeon@gilhospital.com
  • 2Department of Diagnostic Radiology, Gachon University of Medicine and Science, Incheon, Korea.
  • 3Department of Pediatric Surgery, Gachon University of Medicine and Science, Incheon, Korea.

Abstract

Cystic nephroma of the kidney is a rare benign neoplasm that is clinically and radiologically indistinguishable from cystic partially differentiated nephroblastoma and cystic Wilms' tumor. Identifying a cystic nephroma from these neoplastic diseases, particularly with Wilms' tumor, is imperative since the therapeutic strategies differ in these diseases. While cystic nephroma only requires a total surgical resection of the tumor mass, it is strongly suggested to perform a total nephrectomy followed by chemotherapy for the treatment of Wilms' tumor. Since the majority of the renal neoplasm are Wilms' tumors, the possibility of cystic nephroma is often overlooked until a histological confirmation. Therefore cystic nephroma should be considered as a possible diagnosis in cystic renal mass. We recently experienced a case of cystic nephroma which was confused with cystic Wilms' tumor before operation. The cystic renal mass was removed by simple nephrectomy. Five months has passed without any local recurrence since the operation.

Keyword

Cystic nephroma; Nephroblastoma; Wilms' tumor

MeSH Terms

Kidney
Kidney Neoplasms
Nephrectomy
Recurrence
Wilms Tumor
Full Text Links
  • CPHO
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
    DB Error: unknown error