Clin Pediatr Hematol Oncol.
2008 Apr;15(1):33-37.
A Case of Cystic Nephroma in Childhood
- Affiliations
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- 1Department of Pediatrics, Gachon University of Medicine and Science, Incheon, Korea. isjeon@gilhospital.com
- 2Department of Diagnostic Radiology, Gachon University of Medicine and Science, Incheon, Korea.
- 3Department of Pediatric Surgery, Gachon University of Medicine and Science, Incheon, Korea.
Abstract
- Cystic nephroma of the kidney is a rare benign neoplasm that is clinically and radiologically indistinguishable from cystic partially differentiated nephroblastoma and cystic Wilms' tumor. Identifying a cystic nephroma from these neoplastic diseases, particularly with Wilms' tumor, is imperative since the therapeutic strategies differ in these diseases. While cystic nephroma only requires a total surgical resection of the tumor mass, it is strongly suggested to perform a total nephrectomy followed by chemotherapy for the treatment of Wilms' tumor. Since the majority of the renal neoplasm are Wilms' tumors, the possibility of cystic nephroma is often overlooked until a histological confirmation. Therefore cystic nephroma should be considered as a possible diagnosis in cystic renal mass. We recently experienced a case of cystic nephroma which was confused with cystic Wilms' tumor before operation. The cystic renal mass was removed by simple nephrectomy. Five months has passed without any local recurrence since the operation.
