Yeungnam Univ J Med.  2010 Jun;27(1):47-51. 10.12701/yujm.2010.27.1.47.

Anesthetic Management of a Patient with Alexander's Disease: Case Report

Affiliations
  • 1Department of Anesthesiology, College of Medicine, Yeungnam University, Daegu, Korea. adjee@med.yu.ac.kr

Abstract

We present here the case of a 13-year-old male patient with Alexander's disease who underwent surgical correction of a femur fracture. Alexander's disease is a rare and fatal disorder that affects the white matter in the brain and it causes developmental delay, psychomotor regression, spasticity, megaloencephaly and seizure. The patient had the possibility of a seizure attack during the perioperative period. We discuss the anesthetic management of a patient with Alexander's disease and we review the relevant literature.

Keyword

Alexander's disease; Leukodystrophy; Anesthesia; Seizure

MeSH Terms

Adolescent
Alexander Disease
Anesthesia
Brain
European Continental Ancestry Group
Femur
Humans
Male
Muscle Spasticity
Perioperative Period
Seizures
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