J Korean Soc Radiol.  2012 Oct;67(4):293-296. 10.3348/jksr.2012.67.4.293.

Abnormal Positioning of Multiple Abdominal Organs with Anomalous Direct Drainage of Hepatic Vein into the Right Atrium in a Post-Operative Omphalocele Patient: A Case Report

• Hyun SJ
• Cho BS
• Kim SJ
• Lee SY
• Kang MH
• Yi KS

• KMID: 1439544
• DOI: http://doi.org/10.3348/jksr.2012.67.4.293

Abstract

An omphalocele is a rare congenital anomaly in which the infant's intestines protrude through the navel. Additional anomalies that are associated with omphalocele remain present in as many as 50% of cases, and these anomalies vary greatly from patient to patient. However, the persistent anomalies or abnormal position of the abdominal organs in post-operative omphalocele patients have not reported previously. Herein, we report the case of an omphalocele patient with abnormal positioning of the liver, spleen and both kidneys, as well as abnormal drainage of the hepatic vein into the right atrium, which was found during a routine, postoperative follow-up computed tomography scan.

MeSH Terms

Drainage
Follow-Up Studies
Heart Atria
Hepatic Veins
Hernia, Umbilical
Humans
Intestines
Kidney
Liver
Spleen

Figure

• 

  Fig. 1 A 6-year-old girl with a temporary silo placed because of a large omphalocele. A. Initial infantogram on the first day of life. It shows multiple bowel loop herniations into a membrane-covered sac. Radiopaque portion within the sac is thought to represent portions of herniated liver and spleen. B. Follow-up abdomen and pelvis computed tomography 6 years later reveals a craniocaudal liver position. C. Both kidneys are located in just beneath the diaphragm. D. Liver, spleen and both kidneys are shown in the same level, just beneath the diaphragm. The hepatic vein (H) and IVC (I) run to the right atrium, independently. E. Three major hepatic vein show within the liver to form a common trunk. F. Common hepatic vein (white arrow) directly drains into the right atrium, instead of conjoining with the IVC (black arrow). The IVC also drains into the right atrium, independently. Note.-IVC = inferior vena cava, L = left, M = middle, R = right hepatic vein

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