Korean J Radiol.  2008 Jul;9(Suppl):S14-S17. 10.3348/kjr.2008.9.s.s14.

Leiomyosarcoma of the Ovarian Vein: a Case Report with Radiological Findings

• Cho HJ
• Kim HK
• Suh JH
• Lee GJ
• Shim JC
• Kim YH
• Lee HS
• Kang YK

• KMID: 1100096
• DOI: http://doi.org/10.3348/kjr.2008.9.s.s14

Abstract

Leiomyosarcomas of the ovarian vein are very rare. Four cases have been reported in the English language clinical literature. We present a case of leiomyosarcomas where the use of multi-detector CT had a substantial role in the establishment of the preoperative diagnosis. The radiological images as well as intraoperative features are illustrated. We also discuss the radiological findings of the ovarian vein leiomyosarcoma in comparison with those of other venous or retroperitoneal leiomyosarcomas. We expect that the use of multi-detector CT will be the choice for the diagnostic work-up of vascular leiomyosarcomas.

Keyword

Leiomyosarcoma; Retroperitoneal space, neoplasms; Veins, ovarian; Veins, CT; Veins, US

MeSH Terms

Adult
Female
Humans
Leiomyosarcoma/*radiography/surgery
Ovary/*blood supply
Tomography, X-Ray Computed
Vascular Neoplasms/*radiography/surgery
Veins

Figure

• 

  Fig. 1 Radiological and intraoperative findings of ovarian vein leiomyosarcoma in 39-year-old woman. A. Transverse sonography reveals well-defined, spherical, medium-echoic and solid mass with eccentric cystic portion (arrow) at right paravertebral region. B, C. Longitudinal and transverse sonography shows vascular structure, filled with solid components (arrowheads) and connected to main mass (circle), of which superior end shows round protrusion (arrows) in lumen of junctional area of inferior vena cava and right renal vein. D. Just below level of aortic bifurcation, axial contrast-enhanced CT scan shows lobulated and well-defined lobulated retroperitoneal mass with highly enhanced solid components and extensive cystic degenerations (asterisk) at right paravertebral region. E, F. Coronal contrast-enhanced CT scans show vertical pedicular solid structures (black arrowheads), connected to upper portion of mass (circle), which protrudes in lumen of junctional area of right renal vein and inferior vena cava (arrow). Inferior portion of mass connects with normal ovarian vein in pelvis (white arrowheads). G. During surgery, mass (M) is contiguous with right ovarian vein. Note distended right ovarian vein with tumor thrombi (asterisk). En bloc resection of mass together with right kidney, right ureter and retroperitoneal tissue, was performed.

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