Korean J Pediatr.  2005 Jan;48(1):104-107.

A Case of Choledochal Cyst Complicated by Liver Cirrhosis on Pathology in a 20-Month-Old-Girl

• Bae SH
• Choi SY
• Lee TS
• Lee HJ

Abstract

Choledochal cyst is considered to be congenital anomalies of the biliary tract, characterized by varying degrees of cystic dilatation at various segments of the biliary tract. A 20-month-old girl was admitted to Eul-Ji general hospital because of abdominal distension. Physical examination revealed marked splenomegaly and hepatomegaly with nodular surface and hard consistency. Laboratory examination showed elevated transaminase level, alkaline phosphatase level and gamma glutamyltranspeptidase level without evidence of cholestasis. Diagnostic imaging study revealed choledochal cyst with Todani classification type 1. Cholecystectomy and Roux-en-Y choledochojejunostomy was performed, and wedge liver biopsy showed diffuse periportal fibrosis with cirrhotic change and ductular proliferation in the portal area. After operation, hepatosplenomegaly and abnormal laboratory examinations improved rapidly, and in 9 months, the liver and spleen became not palpable. We experienced a case of choledochal cyst complicated by liver cirrhosis on pathology in a 20 month-old girl, and removal of choledochal cyst improved clinical manifestations rapidly.

Keyword

Choledochal cyst; Liver cirrhosis; Child

MeSH Terms

Alkaline Phosphatase
Biliary Tract
Biopsy
Child
Cholecystectomy
Choledochal Cyst*
Choledochostomy
Cholestasis
Classification
Diagnostic Imaging
Dilatation
Female
Fibrosis
Hepatomegaly
Hospitals, General
Humans
Infant
Liver Cirrhosis*
Liver*
Pathology*
Physical Examination
Spleen
Splenomegaly
Alkaline Phosphatase