J Korean Surg Soc.  2013 Dec;85(6):305-308. 10.4174/jkss.2013.85.6.305.

Perineal accessory scrotum with a lipomatous hamartoma in an adult male

• Lee JI
• Jung HG

• KMID: 2212558
• DOI: http://doi.org/10.4174/jkss.2013.85.6.305

Abstract

Accessory scrotum is a rare congenital anomaly that is often associated with perineal tumor or other developmental abnormalities. Because most cases are diagnosed and treated in early childhood, little is known about the natural biologic course of this entity and associated lesions through time. We present a case of accessory scrotum associated with lipomatous hamartoma in a 46-year-old man who was born with a perineal mass. We evaluate the clinicopathologic features and discuss the pathogenesis with a review of the literature.

Keyword

Perineum; Scrotum; Abnormalities; Hamartoma; Lipoma

MeSH Terms

Adult*
Hamartoma*
Humans
Lipoma
Male*
Middle Aged
Perineum
Scrotum*

Figure

• 

  Fig. 1 Macroscopic findings of a perineal mass. (A) Photograph reveals an elongated skin-tag-like protuberance (asterisks) over the round mass (arrows indicate base of main mass). (B) On section, the round mass is composed of yellow adipose tissue. The elongated protuberance has a rubbery texture.

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  Fig. 2 (A) The main mass is composed of predominant mature adipose tissue without atypical cells (H&E, ×100). (B) Small bundles of mature smooth muscle fibers (short arrows) and neural tissue (long arrows) are scattered within the adipose tissue mass (H&E, ×200).

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  Fig. 3 The small protuberance consists of numerous, irregularly oriented smooth muscle bundles beneath the skin, indicating accessory scrotum (H&E: A, ×1.25; B, ×40).

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