J Rheum Dis.  2014 Apr;21(2):77-81. 10.4078/jrd.2014.21.2.77.

A Case of Tjalma Syndrome Coincidentally Accompanied by an Ovarian Teratoma Successfully Treated with Intravenous Immunoglobulin-G Adjunctive Therapy

• Park EK
• Lee SG
• Byon IS
• Lee SH
• Lee SJ
• Nam YJ
• Park JH
• Kim GT
• Park YE
• Park SH
• Lee JW
• Lee JH
• Baek SH

• KMID: 2094661
• DOI: http://doi.org/10.4078/jrd.2014.21.2.77

Abstract

Tjalma or pseudo-pseudo Meigs' syndrome is a clinical condition that is characterized with ascites, pleural effusion, and increased serum CA-125 levels in patients with systemic lupus erythematosus (SLE) without the presence of ovarian tumor. On the other hand, Meigs' and pseudo-Meigs' syndromes represent the same manifestations with ovarian tumor. In this case report, we present a 43-year-old SLE patient suffering from Tjalma syndrome with the coexistence of incidental ovarian teratoma, who was successfully treated with intravenous immunoglobulin-G adjunctive therapy after inadequate response to surgical excision of the ovarian tumor, steroid, and cyclophosphamide pulse therapy.

Keyword

Systemic lupus erythematosus; Intravenous immunoglobulin; Ascites; Pleural effusion

MeSH Terms

Adult
Ascites
Cyclophosphamide
Female
Hand
Humans
Lupus Erythematosus, Systemic
Meigs Syndrome
Pleural Effusion
Teratoma*
Cyclophosphamide

Figure

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  Figure 1. Chest radiograph showing right pleural effusion (arrow).

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  Figure 2. Abdominal computed tomography showing ascites (arrowhead in A) and 4.3 cm sized ovarian tumor (arrow in B).

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