Korean J Oral Maxillofac Radiol.  2008 Jun;38(2):109-115.

Basal cell nevus syndrome: 2 case reports

Affiliations
  • 1Department of Oral & Maxillofacial Radiology, College of Dentistry, Chosun University, Gwangju, Korea. hidds@chosun.ac.kr

Abstract

The basal cell nevus syndrome (BCNS) is an autosomal dominant disorder, characterized by basal cell carcinomas, odontogenic keratocysts and skeletal abnormalities. We experienced two cases that represented several characteristics of BCNS. Case 1: a thirty three year-old man visited CSU hospital. His radiographs showed four cystic lesions at both maxillary sinus and both mandibular angle, with bifid rib and ectopic calcification of falx cerebri. After marsupialization and enucleation, recurrent and newly developing tendency were found on his follow-up radiographs. Case 2: a seventeen year-old man had four large cystic lesions which were diagnosed as odontogenic keratocysts. He had craniofacial anomalies which included ectopic calcification and frontal bossing.

Keyword

Jaw cysts; Basal cell nevus syndrome; Tooth, Impacted

MeSH Terms

Basal Cell Nevus Syndrome
Follow-Up Studies
Jaw Cysts
Nevus
Odontogenic Cysts
Ribs
Tooth, Impacted
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