J Korean Neurosurg Soc.  2013 May;53(5):297-299. 10.3340/jkns.2013.53.5.297.

Pituitary Stalk Hemangioblastoma in a von Hippel-Lindau Patient : Clinical Course Follow-Up Over a 20-Year Period

• Lee KM
• Kim EJ
• Choi WS
• Kim TS

• KMID: 1426198
• DOI: http://doi.org/10.3340/jkns.2013.53.5.297

Abstract

Supratentorial hemangioblastomas (HBs) are rare, and pituitary stalk HBs are extremely uncommon; therefore, pituitary stalk evaluation is often overlooked. Herein, we report the development of pituitary stalk HB over a 20-year period and the importance of regular long-term follow up for patients with HBs.

Keyword

Cerebellar hemangioblastoma; von Hippel-Lindau disease; Pituitary stalk dissemination; Natural course

MeSH Terms

Follow-Up Studies
Hemangioblastoma
Humans
Pituitary Gland
von Hippel-Lindau Disease

Figure

• 

  Fig. 1 Serial magnetic resonance imaging (MRI) of a pituitary stalk hemangioblastoma. A : Sagittal T1-weighted MRI performed 8 years following original resection reveals a normal pituitary stalk. B : Contrast-enhanced sagittal T1-weighted MRI performed 17 years following the initial surgery shows a 5-mm pituitary stalk hemangioblastoma (arrow). C : Twenty-two years following the initial surgery, MRI demonstrates an increased size of the pituitary stalk mass (arrow).

• 

  Fig. 2 Coronal (A) and sagittal (B) contrast-enhanced T1-weighted MRI reveals a thickened edematous optic chiasm (arrow).

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